Hirschsprung ta cuta

Hirschsprung ta cutar tana nufin wani malformation na hagu da rabi na ciwon. An halin babu ganglion Kwayoyin a cikin submucosal da intramuscular plexus. Hirschsprung ta cuta yakan faru a cikin yara a cikin rabo na 1: 5000 lokuta. A matasa, an samu da yawa kasa akai-akai. Boys sha biyar sau fiye da sau da yawa fiye da 'yan mata. Domin wannan pathological yanayin halin da iyalinmu gādo. A wasu lokuta, da cutar da ake dangantawa da bayyanar da Down ciwo. A adult Hirschsprung ta cutar na faruwa a lokacin da yanayin sarrafawa a cikin anorectal yankin. A tsanani lokuta, shi zai iya yada wa distal kananan hanji.

A pathogenesis da cutar taka muhimmiyar rawa da rashin tasirin da parasympathetic rabo daga cikin juyayi tsarin. A sakamakon wannan yanayin ne da bata lokaci ciki sphincter shakatawa dubura, wadda take kaiwa zuwa wani m raguwa a spastic, hanawa na hanji suna, da kuma fa] a] hypertrophy. Asibiti da cutar bayyana a yanayin da aka sani a matsayin megacolon.

Hirschsprung ta cuta na iya faruwa a cika, decompensated subcompensated da kuma siffar. A tsanani daga cikin pathological yanayin dogara a kan anglionarnogo rabo tsawon. Decompensated form aka bayyana tsanani bayyanar cututtuka na ileus.

Halayyar siffofin da cutar ne m zafi, bloating, tsãwa ciki, maƙarƙashiya. Dakata na kujera yana da wani kullum hanya (a wasu lokuta har zuwa wata daya). Bloating ne ma akai alama da cutar, shi ne nauyi da kuma zai iya sa wahala numfashi yaro. Bloating ya zauna ko da bayan wani hanji motsi da taimakon enemas. Its sakamako za a iya kira da bayyanar da m zafi. Babban bayyanar cututtuka da cutar suna a haɗe tashin zuciya da amai, wani rauni, ci deterioration. Matsalolin wannan pathological yanayin ne anemia, nakasawa na line kusassari. A gaban kumburi, ulceration, goiter iya bayar da Yunƙurin zuwa naci zawo cewa sa sha, collaptoid jihar.

Ganewar asali Hirschsprung cutar ta fara da wani gani dubawa. Alama karuwa a ciki saboda da m kumburi, peristaltic contractions da shafi hanji, m stool. Canza ƙanƙancewa na tsuliya sphincter aka ƙaddara ta dijital jarrabawa. Fluoroscopy karkata zuwa ga gaskiya samar da wani fairly m sakamakon. Alama canji a hanji juna saboda kasancewar gagarumin yawa na gas da zai haddasa shãmakacẽwa. A wasu instrumental hanyoyin da ake amfani da ga ganewar asali na pathological yanayi ne colonoscopy, barium enema. A karshen da aka yi amfani da sanin da har da sarrafawa da constriction diamita suprastenoticheskoy ciwon yankin.

Domin tabbatar da ganewar asali da ake amfani da transanal biopsy. Rage neuronal ganglia intermuscular plexus ne mai alama cewa ya tabbatar da Hirschsprung cuta. A lokacin aiki, wannan hanya taimaka wajen sanin matakin na resection.

Jiyya da cutar a jihar ya dogara da tsanani daga tafarkinsa. Cika siffofin za a iya shafe ta da ra'ayin mazan jiya da hanyoyin da far, a wasu lokuta bukatar gaggawa m baki, wanda shi ne don gabatar kolonostomy, cire aganglionarnoy yankin, decompensated, overextension na manyan hanji. Mace-mace bayan gudanar da magani zo har zuwa hudu cikin dari.