Porphyria - wata cuta na zamani mutãne

porphyria cuta ne musamman irin hanta pathologies a kayyade matakin, a cikin abin da akwai cikakken ba daidai ba haemoglobin kira. An yi imani da cewa akwai takwas m ake kira enzymatic matakai a cikin biosynthesis na haemoglobin. Duk wani warwarewarsu a mataki na daya daga cikin su riga kai ga wani matsala kamar porphyria. Cutar yawanci tasowa cikin sauri. A wannan labarin, za mu tattauna mafi daki-daki, abin da yake da wannan cuta da kuma abin da su ne hanyoyin zamani na magani.

Porphyria - wata cuta na zamani mutãne. Mene ne inji na cuta?

Da farko, ba gina jiki na haemoglobin (in ba haka ba - heme) yana tuba a cikin wani mai guba abu wanda, bi da bi, consistently cin bãya cikakken duk subcutaneous nama. Saboda haka, da fata a hankali yakan mallaki wani brownish tint, zama sirara da lokaci, da kuma daga hasken rana kai tsaye bursts. Wannan shi ne dalilin da ya sa marasa lafiya da wannan cuta, za ka iya samun yawa sores kuma scars. Saboda haka a hankali tasowa porphyria. Cuta, mu lura da babu dace magani, yawanci na kama dukan sabon yankunan da fata.

dalilai

Bi da bi take hakkin heme biosynthesis, wanda aka tattauna da ɗan sama, take kaiwa zuwa wuce kima jari na porphyrins a cikin kwayoyin, kazalika da haka ya kira precursors (msl, ALA kuma porphobilinogen). Da shi shi ne na karshe ragi yana da karfi mai guba sakamako a kan kwayoyin, a sakamakon haddasawa riga tasowa na asibiti bayyanar cututtuka. Dalilin irin wannan take hakki ne maye gurbi na gene da alhakin aiki na wasu enzymes da hannu a wani Multi-mataki kira na heme. A lokacin, masana kimiyya suna tsunduma cikin wani karin cikakken nazarin wadannan matakai da wannan cuta a matsayin porphyria.

cuta cututtuka

• Lalacewar da tsakiya m tsarin.
• Fitsari a pinkish ya dafa.
• Wurare da dama a sores da scars a jiki.
• Zafi da rashin jin daɗi a cikin ciki yankin.
• Karuwan jini.

Abin da ya kamata a bi?

Abin baƙin ciki, a wannan lokacin, masana ba zai iya bayar da tasiri hanyoyin da pathogenetic far da wannan cuta. A wasu lokuta (msl, erythropoietic uroporfiriya) magani iya zama mai tasiri. Intermittent porphyria (wata cuta a cikin m mataki) cikakken basa izinin yin amfani da dipyrone da tranquilizers, kamar yadda suka sa a exacerbation na bayyanar cututtuka. A gaban zafi a cikin irin cututtuka kamar porphyria, kamar yadda mai mulkin, Hausa fitar da karfi kwayoyi.

ƙarshe

Porphyria cuta (hoto mai lamba 1 ya nuna daya daga cikin manifestations), da rashin alheri da aka yi fama a cikin wadannan kwanaki fiye da sau da yawa. A ƙarshe, ya kamata a lura da cewa a yau wannan irin cuta har yanzu ya kasance da talauci a san. Masana kimiyya daga ko'ina cikin duniya ci gaba da gudanar da bincike tushen Sanadin, primary na asibiti cututtuka, kazalika da hanyoyin da za a magance irin wannan m matsala. Zauna lafiya!