Kiwon lafiyaCututtuka da kuma Yanayi

Amyotrophic a kaikaice sclerosis: haddasawa, cututtuka, magani

"Amyotrophic a kaikaice sclerosis" Cuta ne mai nauyi kwayoyin Pathology na unknown etiology. An halin raunuka na manya da ƙananan motor neurons, m hanya. Ƙare ALS (amyotrophic kaikaice sclerosis) kokari ne m. Next, mun koyi yadda za a bayyana Pathology, kuma ko akwai wani yiwuwar yin kawar da cutar.

Overview

Amyotrophic a kaikaice sclerosis yana dauke da wani m cutar. Ana rinjayar da tsakiya m tsarin. Pathology yana da wasu sauran sunayen: Lou Gehrig ta cuta, Louis Gehrig ta cuta, misali. A ganewar asali ne ba ko da yaushe sauki. Gaskiyar cewa a cikin 'yan shekarun nan ƙwarai ƙãra kewayon ailments a daban-daban na asibiti manifestations ne kiyaye ba abnormality kamar yadda irin wannan, da kuma amyotrophic kaikaice sclerosis ciwo. A wannan batun, yau masana yi imani da mafi muhimmanci aiki delineation da tsaftacewa cuta etiology.

Amyotrophic kaikaice Sclerosis: Alamun

Bayyananen na Pathology suna hade, da farko, tare da shan kashi na ƙananan motor neuron. Amyotrophic a kaikaice sclerosis, wanda bayyanar cututtuka sun hada da atrophy, wani rauni, fasciculations, yana da ãyõyin lalacewa corticospinal tashar. A karshen ne spasticity kuma Ya ƙãra agara kuma pathological reflexes ba tare da azanci shine hanawa. A wannan yanayin, da cortico-bulbar yankuna za a hannu. Wannan, bi da bi, za ta hanzarta ci gaban Pathology a matakin da brainstem. ALS rinjayar mazan mutane. Pathology ba raya har da shekaru 16.

nuna siffofin

A mutane wahala daga amyotrophic kaikaice sclerosis, farkon matakai na cuta ne alama tsoka atrophy (m hanya) tare da hyperreflexia. Wannan yanayin ne mafi muhimmanci na asibiti bayyana. Pathology iya fara inganta tare da duk striated tsoka zaruruwa. Amyotrophic a kaikaice sclerosis iya samun dama siffofin: bulbar, high, lumbosacral da mahaifa-thoracic. Dalilin mutuwa, kamar yadda mai mulkin, shi ne da shan kashi na numfashi tsokoki bayan game 3-5 shekaru. Amyotrophic a kaikaice sclerosis yana da dama halayyar fasali. Daya daga cikin mafi m manifestations dauke m wani rauni da tsoka zaruruwa na daya daga cikin manya extremities. Yawanci, shi zai fara a cikin wuyan hannu. Tare da ci gaban gyara zubar nama Pathology embodiment kwarara ne mafi m. A farkon cutar hade tare da ci gaban da tsoka rauni a hannu, da aiwatar da hannu thenar zaruruwa. Status nuna wani rauni adduction (shigo) da kuma 'yan adawa na da babban yatsa. A sakamakon haka ne mafi wuya ga fahimci yatsa da kuma forefinger, gaji da damuwa da lafiya motor iko. Marasa lafiya da ALS jin wahala sa (buttoning-saukar) da kuma daukana up kananan abubuwa. Idan rinjayar da rinjaye hannunka bayyana matsaloli a lokacin da rubutu, yau da kullum da ayyukan a cikin gida. In mun gwada m dauke lumbosacral form.

Da hankula Pathology ga

A wannan yanayin akwai wani barga, m da hannu a aiwatar da tsokoki na wannan reshe. Daga baya shi ya fara yada a kan biyu hannun kayar bulbar zaruruwa ko kafafu. Amyotrophic a kaikaice sclerosis iya fara da harshe tsokoki, baki, fuskarsa ko kafafu. A wannan yanayin, da m halaka "da aka ba kamawa up" da asali. A wannan batun, shi dauke da guntu rai expectancy a bulbar form. Marasa lafiya mutu, sauran kusan a kan kafafu, ba jiran ƙananan reshe inna.

kara ci gaba da

Amyotrophic a kaikaice sclerosis tare da daban-daban haduwa daga cikin alamun inna (bulbar da pseudobulbar). Wannan advantageously bayyana dysphagia, kuma dysarthria, kuma daga baya kuma na numfashi cuta. A halayyar alama na kusan dukkan siffofin cuta an dauke su wani wuri karfafa da muƙamuƙi reflex. Lokacin da hadiya da ruwa abinci dysphagia lura mafi akai-akai fiye da da daskararru. A lokaci guda, ya kamata a lura da cewa yin amfani da karshen a cikin shakka daga cuta ci gaban zama mafi wuya. Akwai rauni a cikin masticatory tsokoki, yana farawa drooping taushi palate, da harshe zama atrophic kuma gyarawa. Amyotrophic a kaikaice sclerosis farawa tare da wani ci gaba da kwarara na yau, anarthria. Yana zama ba zai yiwu ba ta hadiye, ta qara da alama na tsammãni ciwon huhu. Ya kamata kuma a lura da cewa cramps (intermittent cramps a cikin 'yan maruƙa) da aka ruwaito a dukan marasa lafiya, da kuma sau da yawa yana dauke da farko alamun cutar.

Rarraba atrophy

Zan iya cewa, shi ne wajen zabe. A cikin hannãyenku daga cikin haƙuri Notes kashi hypothenar, thenar, interosseous da deltoids. Kan kafafu atrophy tasowa a fannonin yin lankwashewa zuwa baya. Na bulbar tsokoki lalace nama da taushi palate da kuma harshe. Oculomotor zaruruwa suna dauke da mafi resistant zuwa atrophy.

m lura

A Pathology na rare da sphincter cuta. Daya daga cikin ban mamaki siffofin da cuta ne da rashin matsa lamba ulcers a shanyayyen na dogon lokaci bedridden marasa lafiya. Har ila yau, shi ya gano cewa gigin-tsufa faruwa a lokacin da cuta ne musamman rare. Fãce imani kawai 'yan sub-kungiyoyin: da iyali da kuma hadadden tsari "parkinsonism-gigin-tsufa AD sclerosis." Bayyana a matsayin lokuta shafe wata uniform ƙananan ko babba motor neurons. Wannan na iya fi kayar da wani daya yankin. Alal misali, sama da mota neuron iya shan wahala karfi. A wannan yanayin da muke magana na farko a kaikaice sclerosis. Tanƙwasãwa lalacewa za a iya lura a cikin ƙananan motor neurons. A wannan yanayin da muke magana na perednerogovom ciwo.

rheotachygraphy

Wannan hanya ne na musamman bincike darajar tsakanin paraclinical hanyoyin da karatu cuta. Da taimakon electromyography saukar tartsatsi lalacewar da agara Kakakin sel (ciki har da waɗanda suke a cikin ceto (asibiti) tsokoki) tare da fasciculations fibrillation, canje-canje a cikin mota naúrar iko, m kalaman a kan bango na al'ada gudu daga yaduwa daga zumudi tare da zaruruwa a azanci shine jijiyoyi.

bincikowa da

Don gudanar da bincike domin gano Pathology, dole ne ka yi:

  • Ãyõyin lalacewar da ƙananan motor neurons. Wajibi ne, musamman, da kuma EMG tabbatarwa ceto (asibiti) tsokoki
  • Alamun babba motor neuron lalacewa a m hanya.

Ga ganewar asali dole ba:

  • Sphincter cuta.
  • Azanci shine disturbances.
  • Parkinson ta cutar.
  • Kayayyakin hanawa.
  • Bass mimic manifestations.
  • Gigin-tsufa na Alzheimer irin.
  • Autonomic cuta.

Ganewar asali aka tabbatar fasciculations a 1 ko fiye zones, EMG alamu al'ada gudun yada wani zumudi azanci da kuma mota zaruruwa. Daga cikin Categories kamata a lura:

  • M tare da ALS. A hali a aya ta zo gane alamun rauni a cikin ƙananan motor neurons da kuma saman uku yankunan na jiki.
  • M. A wannan yanayin, akwai alamun wani rauni a cikin ƙananan kuma babba motor neurons kuma a yankuna biyu na jiki.
  • Zai yiwu. Raunuka nuna alamun manya da ƙananan motor neuron a daya yankin na jiki ko a lalace a karo na biyu zones 2-3. A karshen harka muna magana ne game da manifestations ALS a daya reshe, m bulbar palsy da primary form.

Jiyya na amyotrophic kaikaice sclerosis

Yau na farko da kawai miyagun ƙwayoyi amfani a Pathology, shi ne wajen "Riluzole". An amince a Turai da Amurka, amma a Rasha ba rajista da kuma ba za a iya shawarar da na aikin likita. Magani ba kawar da cutar. Amma shi ne kawai miyagun ƙwayoyi da cewa yana da kyau sakamako a kan rayuwar jama'a da marasa lafiya. A medicament "Riluzole" taimaka rage taro na glutamate (neurotransmitter a CNS), saki a lokacin da nassi daga wani jijiya turu. An wuce haddi na wannan fili da aka samu a cikin lura hallakaswa ayyukan a kan kashin baya neurons da kuma kwakwalwa. Bisa ga sakamakon asibiti karatu gano cewa, waɗanda suka riƙi magani, ya rayu wani talakawan of 2-3 watanni fiye da wadanda suka yi amfani da wani placebo.

antioxidants

Wannan aji na mahadi gina jiki taimaka hana lalacewar da jiki da za su iya haifar da free radicals. An yi imani da cewa wani mutum da ALS iya zama mafi saukin kamuwa zuwa ga mummunan tasiri. Yau, nazarin ne underway su gane, gane da amfani effects kari dauke da antioxidants. Wasu daga cikin wadannan kayayyakin sun shũɗe da gwajin, ya kasa tabbatar da ingancinta.

concomitant far

Ayyuka daban-daban taimake yin rayuwa sauki ga marasa lafiya da su sa shi ya fi dadi. A musamman, muna magana ne game da shakatawa. An yi imani da cewa reflexology, aromatherapy kuma tausa taimaka kashe danniya da kuma rage tashin hankali, shakata tsokoki, da daidaita jini da kuma Lymph wurare dabam dabam. Wadannan hanyoyin taimaka wa rabu da mu da zafi saboda da kira na na ciki zafi kisan samar da jiki da kuma endorphins. Ko da magani ko kuma wani hanya ya kamata a shawarar da wani likita. A amyotrophic kaikaice sclerosis kai-magani ba sosai shawarar.

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