Kiwon lafiyaMagani

Batalov bututu. Kogon Batalov bututu. Nakasar zuciya cuta

mutum jinin samar tsarin hada da wani babban jiki, da zuciya da kuma arteries tafi, dawo daga jijiya nama. Its daidai aiki ne saboda al'ada anatomic tsarin da hemodynamic yanayi. A hali na take hakkin daya daga wadannan yanayi biyu ya auku, da kuma lalata zuwa wasu gabobin da jinin samar.

topicality

Abin baƙin ciki, da abin da ya faru na nakasar malformations da dukkan girma a kowace shekara. Wannan shi ne saboda da farko da tabarbarewar muhalli da yanayi da kuma kiwon lafiya ko rashin amfani da iyaye. Yadda za a koyar da pediatricians, shirya domin haihuwar jariri, ya kamata a fara tun yana karami,, game da shi yana ambaton cewa duka maza a tsarin iyali ya kamata a hankali kula da kansu. Saboda haka, na dogon lokaci kafin daukar ciki ya bari miyagun halaye, to warkar da kullum cututtuka, expectant uwa - wa gyara gani, abinci, normalize hutu. Duk da haka, shi yake faruwa, da kuma lokuta kamar a wani m iyali, yara suna haife tare da nakasar malformations. Sabõda haka, a matakai daban-daban na gestation mace da sha na lokaci-lokaci duban dan tayi za su iya gane a utero fetal cuta. Amma ko da irin wannan bincike tsari ba nufa da bukatar zubar da ciki, bayan duk, magani ba ya tsaya har yanzu, kuma yanzu yawancin haihuwa lahani bi. Wata irin wannan misali ne mai haske jijiya kogon (Batalov) bututu.

kwarara da ayyuka

A tsarin na fetal jini ya kwarara ne muhimmanci daban-daban daga abin da ya fara tasawa. Wannan shi ne saboda ta musamman da iko a utero - ta hanyar mahaifa daga cikin uwa tasa ta jini a nasa jini ya sami dukan zama dole domin ci-inganta abubuwa, ciki har da oxygen. Kuma saboda da bukatar numfashi da kuma narkewa kamar tsarin, domin lokaci kafin haihuwa ne kawai ba na nan, yayin da zuciya da jijiyoyin jini tsarin ne a gaggawa yanayin. Daya daga cikin mafi muhimmanci su ne siffofin da m taga a cikin atrial septum, kuma Batalov bututu. Tare da taimakon da karshe lakã an haɗa zuwa akwati na huhu jijiya, kuma haka mahaifiyar ta jini ka kewaye da na huhu jijiyoyin bugun gini da dama a cikin wani babban da'irar fetal wurare dabam dabam. Yadda aka saba, a cikin farkon hours na baby ta rayuwa idan mike cikin huhu, kuma ya fara numfashi a kansa, ya kamata stenosis, kuma a lokacin farko da kwanaki - gaba daya shãfe gani da kuma ya juya a cikin wani gungu. Duk da haka, idan wannan bai faru, kuma ya zauna bude Batalov kwarara, to, akwai mai tsanani hemodynamic disturbances a cikin jini zagayawa tsarin na yaro.

etiology

uku manyan dalilan wannan malformation za a iya bambanta. Farko - wannan shi ne wani nakasar abnormality, wanda hadawa bude Batalov bututu, misali Down ciwo da kuma tetralogy na Fallot. Na biyu - mai nauyi a lokacin haihuwa da rikitarwa, abu don hypoxia ko fetal asphyxia. Yana iya zama da slowness, shafe tsawon tsaye na shugaban sama ƙofar kafafuwa, wanda bai kai ba katsewa na membranes, abin da ya faru na hawa kamuwa wuyansa igiyar katsalandan ko overlapping airway fetal membranes da yawa wasu. Kuma a karshe, na uku - shi ne mai ban mamaki, watau, utero kafa abnormally fadi ko tsawo Batalov kwarara saboda da tasiri dalilai daga uwa zuwa da yaro a lokacin da alamar shafi zuciya, cewa shi ne, a cikin ta farko 10 makonni na ciki. Saboda haka, teratogenic mallaka da yawa da kwayoyi, musamman hormones, hypnotics da kuma maganin rigakafi, da ƙwayoyin cuta, barasa, shan taba, danniya yanayi. Amma har zuwa wannan lokaci, wata mace ya kamata a kewaye da m da kuma a Jihar ta jiki da kuma Psycho-wani tunanin sauran.

pathogenesis

Hemodynamic disturbances a cikin wannan nakasar zuciya lahani, kamar kogon Batalova bututu an sa da farko sallame na jini daga lakã da na huhu akwati saboda da bayyana matsin lamba dan tudu. Saboda haka, da na huhu wurare dabam dabam da aka dora kuma shi hankali tasowa stasis bi ta exudation daga cikin ruwa wani ɓangare na jini a cikin kewaye nama. Huhu zama sauƙi saukin kamuwa zuwa cututtuka, zama kasa yadda ya kamata wadãtar da jini tare da oxygen. A lokaci guda, ta rage ƙarar na zagawa da jini a babban da'irar ne ta? Ãr, duk da gabobin Ana rinjayar da tsanani hypoxia, kazalika da jikin wani jariri a farkon shekara murtuke zuwa a kalla tsanani, suka bukatar da yawa sosai gina jiki da kuma samar da makamashi. Kuma saboda girma karancin su dystrophy, sakamakon wahala da su aiki. Baby samu nauyi sannu a hankali, sau da yawa rashin lafiya, ya zama m, kullum suna ihu.

aiki

Duk da haka, lura da wannan cuta ba sai wuya, saboda kawai matsalar da ya rage bude Batalov bututu. The aiki ne kawai daya daga da magani, saboda ra'ayin mazan jiya hanyoyin kada ku yi a kan shi. Yi m aibi gyara ne yawanci 5-10 shekaru, amma mafi kyau shekaru domin wannan yana dauke su 3-5 shekaru. Babban abu da ya faru kafin balaga, lokacin da yana da hormonal reorganization na wani kwayoyin, kuma shi zai bukatar karin jini wadata. Akwai shaida da ya zama ruwan dare lokuta da magani cikin adulthood bayan marigayi ganewar asali da mataimakin. A lokacin aiki Batalov bututu kawai sutured ko ligated chressosudistym damar daga femoral jijiya zuwa ga mafi karami rauni baby kyallen takarda. Duk wannan ya faru karkashin iko angiography kuma da taimakon endoscopic na'urorin. Wannan mini-aiki ne rayayye ci gaba da likitoci da kuma ba wuya.

Outlook

Bayan da magani, da cutar yana da wani m sakamako, da rayuwa Hasashen ne yawanci ba ya canzawa. Yana dogara a kan mataki na aibi diyya idan aka gano da kuma mataki na canje-canje a cikin jijiyoyin bugun gini tsarin na cikin huhu. A hankali, duk da haka, wadannan marasa lafiya da m zuciya rashin cin nasara, sau da yawa wuya ta infective endocarditis. Ya bayyana guda hali a lokacin da neprooperirovannye marasa lafiya rayu zuwa 70-80 shekaru, saboda kananan sabawa na ductus arteriosus kuma mai tsanani compensating ikon da kwayoyin.

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