Kiwon lafiya, Cututtuka da kuma Yanayi
Farah cuta. Haddasawa, ganewar asali, magani
Farah ta cuta da aka farko da aka bayyana a cikin 30s karni na ashirin da. Wannan sigar gaji cuta (cerebral jijiyoyin bugun gini calcification). A mafi yawan lokuta don haka ya kira kungiyar na pathologies a cikin abin da ya shafa yankuna na kwakwalwa da kuma jini. alli salts ake ajiye a cikin ganuwar kananan jijiyoyi, capillaries. Farah ciwo ya auku a kusa da shekaru 40-50 shekaru, amma akwai lokuta, da kuma a baya ta manifestations.
A rukuni na neurodegenerative cututtuka
Wannan rukuni na cututtuka da halin tsakiya m tsarin. A wasu yawan neurons mutu, wadda take kaiwa zuwa neurological cuta. Neurodegenerative cututtuka zai iya samun daban-daban haddasawa da kuma daban-daban na asibiti manifestations. Yana da muhimmanci cewa duk cututtuka a cikin wannan category ne m. All far, wanda aka yi amfani, ne symptomatic. Wannan shi ne, shi facilitates bayyanuwar da cutar, amma ba da taimako zuwa ga farfadowa daga lalace yankunan. A mafi tasiri zai zama na tsarin jijiya nama dasawa, duk da haka, hanya yana da biyu fasaha da kuma halin kirki cikas. Domin irin wannan cututtuka sun hada da Alzheimer ta cuta, Parkinson, Farah. Yawanci, ganewar asali da cututtuka a farkon matakai utrudnena. Mafi sau da yawa a cikin ganewar asali da masana dangane da haƙuri gunaguni da kuma lura da ayyukansu. Amma babban kayan aiki ne a scan (lissafta, Magnetic rawa).
symptomatology da cutar
Tun da cutar - a rare sabon abu, da masana da wuya don samar da daidai asibiti hoto na ciwo. Alamun iya faruwa idan haƙuri ne girmi shekaru 40. A ƙaramin mutane Fara bayyanar cututtuka da cutar iya Heart da indistinct. Marasa lafiya gaji da damuwa da daidaituwa na ƙungiyoyi, parkinsonism. Har ila yau a ci gaba da cuta na iya nuna bayyanar cututtuka irin su tremor, dystonia, m kuma sababbu reshe ƙungiyoyi (chorea), involuntary contractions daga cikin hannãyenku, ƙafa. Tun da cutar rinjayar yankunan na kwakwalwa, da rage aiki iya aiki, da iyawarsa ta tunani. Har ila yau, shan wahala da memory na mutum. Sau da yawa keta da shi. Sauran neurological ãyõyinMu su hada zafi, shafi tunanin mutum cuta. Bambanta da na yara nau'i na cutar, wanda bayyana kanta a yara, matasa. Babban bayyanar cututtuka a cikin wannan yanayin ne kamar haka: dystonia, chorea, seizures na epilepsy. Na tsufa nau'i ne halayyar ga tsakiyar da kuma mazan shekaru. A wannan yanayin, akwai parkinsonism, jawabin cuta, wasu matsaloli a cikin juyayi tsarin. Ma yana iya zama urinary incontinence.
Yiwu haddasawa na ciwo Farah
A dalilan saboda wanda zai iya ci gaba da cutar da aka ba da kafa. Duk da haka, an san cewa wata babbar tasiri a kan ta fitowan ne cuta na thyroid, parathyroid gland. Lokacin da kasawa faruwa a cikin wannan musayar aiwatar alli, phosphorus. Irin wannan neurodegenerative cututtuka na iya faruwa a cuta da acid-balance tushe a cikin jiki. Alkalosis, abu don wani gagarumin asarar acid. Amma da alkaline fili ba a wuce haddi. Akwai kuma view cewa ciwo da aka bayyana a cikin Farah kwayoyin cuta. Wannan ne mutated gene cewa shi ne alhakin musayar irin wannan abubuwa a matsayin alli. Duk da haka, wannan version yana da yawa saba wa juna. Known ware lokuta, a lokacin da bayyanar cututtuka da cutar bayyana bayan sakawa a iska mai guba na kai, dalma da gubobi, gubar, a yara da Down ciwo. Har ila yau, calcification aka gane a cikin mutane, rubella (m). Wani zai yiwu hanyar calcification na muhimmi ganglia - haihuwa raunin.
bincike da hanyoyin for ganewar asali
Kafin fitowar CT marasa lafiya underwent radiological nazarin kwakwalwa. Godiya ga zuwan hanyoyin zamani na bincike, masana sun samu mafi m images daga shafa yankin. Duk da haka, ya kamata a lura da cewa mafi girma ji na ƙwarai ga wani ba na asibiti hoto yana kwamfuta, maimakon Magnetic rawa Dabarar. A cikin bincike na masu rinjaye na hotuna shafi yankunan an iyakance ga wani kodadde sarari suKe. Su ne a cikin kananan size. Mafi sau da yawa sha canje-canje a cikin muhimmi ganglia, thalamus, cerebellum. A matakin na calcification a kusa da wannan da cewa matasa da cewa a cikin tsofaffi. bambance-bambance ma aka samu tsakanin kungiyoyin, a cikin abin da cuta ne asymptomatic Farah, da kuma waɗanda inda ciwo yana tare da furta bayyanar cututtuka.
histological nazarin
A lokacin gwaji kan gawar jarrabawa a cikin kwakwalwa halin da ake ciki shi ne kamar haka: tasoshin da whitish bayyanar (wasu sashe shafukan). Lokacin da taba da wuka da suka yi sauti kamar crunch. Domin histological bincike na biopsy samfurori da aka yi: The sassan na cerebral bawo, muhimmi ganglia, cerebellum. Yana da yake a karshe calcification auku mafi sau da yawa. The samfurori da alli salts ba. Har ila yau, mafi sau da yawa suna gano a cikin jijiyoyi (kananan, matsakaici), da capillaries. Kadan na kowa (harben lokuta) cuta Farah hits jannayẽnsa. Cikin dukanin tsawon tasoshi, kazalika a cikin kewaye kyallen takarda gano alli conglomerates a kananan masu girma dabam. Har ila yau a cikin kyallen takarda ware gaban burbushi na arsenic, aluminum, cobalt, mucopolysaccharides.
ganewar asali
Dangane da ko da cutar bayyanar cututtuka na Farah, da lifiya iya utrudnyatsya yan. Sau da yawa shi ne kamu kwatsam, jawabin da Dabarar tabbatar da wani gaba ɗaya daban-daban cutar. Da farko, da gwani ba ya karya da metabolism na alli da sauran malformations. Sa'an nan sanya lissafta tomography (ko X-ray Nazarin). Doctors lura cewa daya daga cikin matsalolin da a daidai ganewar asali ne hypoparathyroidism. Da cutar, wanda ya auku a lokacin da rashi na parathyroid hormone. Saboda haka, da jini alli matakin saukad, da phosphorus matakin na karuwa ne. Idan CT scan an kiyaye calcification striopallidozubchatyh Tsarin, sa'an nan a rarrabe hypoparathyroidism daga wani yanayin kamar cuta Farah, ƙarin ƙididdiga. Da farko, yana da muhimmanci domin sanin matakin na parathyroid hormone da alli. Kuma yi amfani da ganewar asali parasitic shan kashi na juyayi tsarin. Specific halayen da faruwa a cikin jini, cerebrospinal ruwa. Infrequently, cutar headlamp bambanta da irin wannan yanayin kamar yadda Bourneville sclerosis.
magani
Ana cire alli yawa, wanda aka kafa a cikin kwakwalwa da jini, shi ne ba zai yiwu ba. Matsayin mai mulkin, da lura da wannan cuta ne symptomatic. Da farko, shi ne da nufin kyautata metabolism na alli da phosphorus a cikin jiki. Idan cututtuka ne kiyaye Parkinson ta cuta, da gwani ya furta musamman kwayoyi (levodopa). Farah ma cuta, da magani daga ta bayyananen, ya shafi ci daga antioxidants, jamiái domin inganta metabolism. Jiyya na alli tashar blockers ne m. Yana da daraja idan akai la'akari da gaskiyar cewa cutar ne a rare da talauci gane. A mafi yawan lokuta, far ne don ya rage bayyanar cututtuka manifestations da cutar, amma da mataki na calcification ba ya canzawa.
Tsinkaya a cutar headlamp
Tun da yake wannan yanayin warware da metabolism na kwakwalwa, kazalika da alli salts da wani sakamako a kan irritating ta nama, cutar Farah kintace ne wajen shubuha. Cutar progresses sannu a hankali tare da shekaru, alli adibas kara. Hakika, duk wannan ba ya faruwa a shekara guda. Kullum, neurodegenerative cututtuka ci gaba a kan da dama da suka gabata. Babban matsalar shi ne rashin bayani a kan jihar, kazalika babu takamaiman magani. Saboda haka, far ne da nufin kyautata ingancin rayuwa na haƙuri. Wani mummunan nufi - bad cutar da ake bincikar lafiya a farkon matakai.
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