Hemosiderosis na huhu: Bayyanar cututtuka da kuma magani

Hemosiderosis na huhu - wani ƙwarai da gaske cuta. Yana faruwa a lokacin wani taro na ja da maikacin jini a lamba tare da nama na mutum huhu. A lokacin da wannan ci gaba na dogon lokaci da ci gaban hemosiderin pigment dauke da baƙin ƙarfe.

Mene ne hemosiderosis?

Don gane asali da wannan cuta mai yiwuwa ne kawai a kan tushen da X-ray, duk da haka, akwai mutane da yawa cututtuka ga wanda da kasancewar za a iya zaci. Rarrabe ãyõyi, mãsu haƙuri gemosiderkoz huhu - wani mummunan tari, hawking up zuwa jini, shortness na numfashi, zub da jini a cikin huhu. Akwai iya zama da zazzabi da kuma tachycardia.

A kan tushen da X-ray na huhu likita zai iya yi wani tabbataccen ganewar asali. sauran karatu ne ma gudanar da su tabbatar da cewa haƙuri yana fama da wannan cuta ne. Shi ne da jarrabawa na sputum, jini sunadarai, a mai tsanani lokuta - huhu biopsy.

Jiyya da cutar samar da aikace-aikace na corticosteroids da kwayoyi da kashe takamaiman bayyanar cututtuka.

bayyanuwar cuta

Idiopathic na huhu hemosiderosis kuma ake kira ciwo m-Gellerstedta. Wannan shi ne wani pathological matsalar, wanda bayyana kanta a matsayin sakamakon wani musamman pigment hemosiderin shaida a mutum huhu. A babban alama wannan pigment a gaskiyar cewa shi kunshi baƙin ƙarfe oxide. Shi ne ke da alhakin ajiya na baƙin ƙarfe a cikin jiki. A lokacin da cututtuka daban-daban shi accumulates a cikin kyallen takarda, wadda take kaiwa zuwa haƙuri da kiwon lafiya da matsaloli. Har ila yau, ana iya tara a jikin mutane.

A da ginshikin, hemosiderin - siffofin adana a cikin jiki kayayyakin baƙin ƙarfe. Saboda wannan masana'anta da furta m ya dafa. Lokacin da wani mutum tasowa idiopathic na huhu hemosiderosis, a cikin tsokoki na jiki za su tara har zuwa biyar grams na baƙin ƙarfe.

By kanta da baƙin ƙarfe jari ba dole ba ne shafar aiki na asali abubuwa na jiki, a wannan yanayin da huhu. Duk da haka, idan tare da na huhu hemosiderosis sclerosis, da aikin cuta a cikin jikin makawa.

A hadarin marasa lafiya mai saukin kamuwa da wannan cuta ne matasa da yara da kuma matasa. More sau da yawa fiye da mata.

A Sanadin cutar

Hemosiderosis na huhu na iya faruwa a cikin mutane domin daban-daban dalilai. Mafi na kowa - da wani nakasar lahani a cikin jirgin ruwa ganuwar da na huhu wurare dabam dabam. Saboda wannan, a cikin jiki akwai wata ãr na capillaries da kuma wucin gadi lõkacin fatara daga jini ya kwarara. Saboda haka exuded erythrocytes, kuma a cikin huhu kyallen takarda ne m huhu microbleeds.

A sakamakon wannan baƙin ƙarfe da aka saki da kuma da dama a cikin hemosiderin. Ya, bi da bi, da ake tunawa da alveolar macrophages da kuma ajiye a cikin epithelia da endothelial Kwayoyin a babban wuce haddi. Har ila yau taka banrazana rawa ne wani nakasar lahani. M dangane tsakanin biyu jikinsu, a cikin wannan harka - da Bronchial arteries da jijiyoyinmu daga cikin huhu.

Immunoallergic yanayin da cuta

Sanadin da morphogenesis na huhu hemosiderosis iya zama immunoallergic. Lokacin da wannan rigakafi gidaje sa lalacewar da babban ganuwar da na huhu capillaries. Akwai take hakkin su da al'ada aiki, ta hanyar da lalace jini a cikin huhu da dama da suka wuce haddi baƙin ƙarfe, sakamakon jiki na yin aiki tsanani gaji da damuwa.

Har ila yau, wuce kima shaida na hemosiderin a cikin huhu nama na taimaka wa m aiwatar da lalata ja da maikacin jini, tare da sakin haemoglobin, wanda ya auku a cikin baƙin ciki. A high matakin na baƙin ƙarfe sha a cikin Gut, tsawo da yin amfani da kwayoyi da wani babban baƙin ƙarfe abun ciki.

A can farko na huhu hemosiderosis a yara na iya faruwa a matsayin idiopathic cutar da cewa ba a hade da wasu matsaloli. A iya tare da ciwo Gainer (a cikin akwati idan jiki ne ma kula da sunadaran kunshe ne a cikin halitta Bovine madara).

Idan hemosiderosis faruwa sake, da huhu mikrokrovotecheniya iya kai wa ga hawan jini, wanda zai iya zama na kullum matsala.

Har ila yau, cutar na iya a tare da da ciwo na Goodpasture. Wannan shan kashi na Alveoli daga cikin huhu da kuma kodan, tare da su scarring. A cuta ne yawanci batun maza masu shekaru 20 zuwa shekaru 30. Akwai wani ra'ayi game da hereditary yanayi.

m hemosiderosis

Idiopathic na huhu hemosiderosis a yara ne sau da yawa jawo by cututtuka. Yana iya zama kamar yadda sauki SARS, kazalika da mafi tsanani cuta - kyanda, whooping tari da zazzabin cizon sauro. Har ila yau, shi zai iya zama sakamakon buguwa.

M hemosiderosis tasowa a kullum zuciya matsaloli. Yana iya zama kowane irin cardiac cuta - zuciya cututtuka, cardio da kuma sauran cututtuka.

M haddasawa maimaita kuma m hemosiderosis protrude tsawo daukan hotuna a low yanayin zafi, karfi na jiki ko shafi tunanin mutum da iri, amfani da wasu magunguna.

Idan hemosiderosis gudana a ciki da Alveoli daga cikin huhu, cewa hotunan fili bayyane burbushi na microbleeds da wuri wuce kima adibas na hemosiderin ne kama da nodules, wanda aka shirya daga cibiyar ga periphery daga cikin huhu.

cututtuka

Hemosiderosis na iya faruwa a dama siffofin. M, subacute kuma maimaita. Idan cutar da ake gani a yara, mafi sau da yawa shi ya auku a farkon makarantan nasare shekaru, tun shekaru uku. Duk da haka, akwai marasa lafiya a wanda ganewar asali ne ya sa a farko makonni na rayuwa.

Bayyana cutar huhu hemorrhage da kuma zub da jini, ji na numfashi gazawar.

A lokacin da ya faru na da rikitarwa a cikin mutane bayyana nauyi tari m launi, a mai tsanani lokuta, za a iya coughing sama da jini. A matasa da yara, da jini zai iya zama a cikin aman.

A jarrabawa, likitoci kula wheezing, tachycardia, zazzabi, sau da yawa haƙuri tanã kai ƙãra jin zafi a kirji da ciki, kazalika a gidajen abinci. Yana iya kuma zama mahaukaci kara girma na hanta da kuma kaifi digo a cikin nauyi.

Idan hemoptysis ci gaba na dogon lokaci, da mãsu haƙuri tasowa anemia, wani rauni da juwa. A fata ya zama kodadde, da kuma a kusa da idanu akwai wata xabi'a yellowness. Mutumin da gaji da sauri da kuma ci gaba da jin wani amo a kunnuwa. Tã lokaci da cutar na iya faruwa daga 'yan sa'o'i 10-15 kwanaki. Saboda haka, akwai ba zai iya yi ba tare da kiwon lafiya.

A lokacin da worsening tari, kuma shortness na numfashi zai iya rage, amma yana da wuya ba kwarin gwiwa, ganin likita ake bukata nan da nan. A korafin gafarta musu ba a samuwa a duk, da kuma mutum zai iya kai cikakken rayuwa aiki wanda ake iya yi.

Tare da kowane exacerbation da cutar gafarar lokaci an rage, amma rabo ƙara da tsawon da kuma tsanani daga crises. Daya daga cikin illolin anemia - jimlar ãr na jiki. A rare lokuta, ko zai yiwu mutuwa na haƙuri - wani bakin ciki sakamako zai iya faruwa saboda m huhu hemorrhage kuma kwatsam numfashi gazawar.

ganewar asali hemosiderosis

Domin a daidai gane asali na huhu hemosiderosis, kana bukatar wani gwani ra'ayi da dama masana. Da farko, yana da pulmonologist, hematologist. Kuma ma bukatar karatu na asibiti manifestations da cutar. Ba za a iya yi ba tare da nazarin X-haskoki, sputum analysis, jini (kamar yadda wani janar analysis, da kuma biochemical) da kuma huhu biopsy.

Don gane asali da wannan cuta ne musamman wuya. Sau da yawa dauki watanni ko ma shekaru, kafin masana suka gano wata ganewar asali. Wani lokacin sa shi posthumously. The abu ne cewa, na farko shi ne ba takamaiman bayyanar cututtuka, kama da yawa da sauran cututtuka, da kuma da yawa kawai ba ba su darajar. Yawancin dai kawai wani numfashi rashin lafiya tare da tari da anemia.

m zamani

Idan likitoci suka kamu da idiopathic na huhu hemosiderosis, magani ne na wajibi. Jiki da kanta ba zai iya jimre wannan matsala. A cikin m nau'i na cutar da ake tare da crackles da palpitations. A lokaci guda rage matakin na ja da maikacin jini, dagagge bilirubin matakan da magani baƙin ƙarfe a cikin jini ne kadan.

A lokacin crises faruwa leukocytosis, ESR matakin fito, wanda yawanci nuna kumburi. A baya, saukarwa da cutar bayyana polycythemia. Shi ne mai kirki da ƙari tsari, tare da hyperplasia na bargo Kwayoyin.

X-ray nazarin

A cikin nazarin X-haskoki a farkon matakai da cutar halin da rage na gaskiya daga cikin huhu filayen. A daidai wannan lokaci, a kan uku da na hudu, saukarwa ne ya lura da zafin duhun da raunuka na connective nama tare da halayyar scars.

Sau da yawa akwai sabon mai da hankali inuwa, duk da cewa tsohon bace. A spirography bayyana numfashi wuya, a kan electrocardiogram - miokardiostrofiya. Karshe ganewar asali taimaka huhu biopsy.

hemosiderosis magani

Nasara lura da wannan cuta ne kawai zai yiwu a lokacin da dadewa magani darussa na corticosteroids. Alal misali, "Prednisolone" taimaka warkar da na huhu hemosiderosis. Da miyagun ƙwayoyi minimizes da permeability na jini da kuma inhibits da ci gaban autoimmune halayen.

Idan ra'ayin mazan jiya jiyya da ake gane zama m, sa'an nan m hanyoyin da ake amfani da su. Iya cikakken ko partially kawar da baƙin ciki, da shi za a iya rage hadarin remissions. Har ila yau yana rage alama na crises, da kuma haƙuri da rayuwa Hasashen bayan wannan aiki zai kara da 7-10 shekaru.

Shirye-shirye a cikin m lokaci na cuta ci gaba

Abin lura shi ne cewa a cikin m lokaci da kuma a cikin rigakafin kama kwayoyi wajabta. Lokacin da ganewar asali "na huhu hemosiderosis" zalunta hali yadda ya kamata ta hanyar hade da cytostatic jamiái da plasmapheresis. Wannan rage bayyanar sabon autoantibodies da kuma taimaka jiki jimre da haihuwa.

Haka ma, wani tasiri Hanyar - kau na baƙin ƙarfe a cikin fitsari, da ake amfani da wannan jiko "Desferal". A lura da cututtuka amfani bronchodilators, antikoagulyarnye nufi.

Dogon lokacin da gafarar likitoci za su iya cimma, yayin da mutunta su da marasa lafiya a tsananin rage cin abinci cewa zame duk kayayyakin bisa saniya ta madara. Idan cutar ta gudana a cikin kullum mataki, watakila da nada nitrates. shi ne musamman hade da na kullum zuciya matsaloli.

iri hemosiderosis

Likitoci ne dama irin wannan cuta. A musamman, na huhu hemosiderosis halin (macropreparations "Brown induration haske"). A wannan yanayin, da huhu kara a size, da sosai m texture. Har ila yau, duhu-ja zuwa launin ruwan kasa a kusa da kan bangaranci m whitish Layer da brownish inclusions.

Yana iya faruwa hemosiderosis huhu (micropreparations № 111). A wannan yanayin, ruwan kasa pigments a bayyane a cikin sel da kuma waje da cewa a lokacin awon dauki Perls zama blue ko greenish. Sun bayyana tsakanin bronchi da Alveoli cavities.

Bugu da ƙari, waɗannan kwanoni ne mutum huhu ne musamman kara girman da cunkoson ababen hawa. Cutar da ake tare da m zub da jini a bangare tsakanin Alveoli. A lokaci guda suna gano Layer na connective nama.