Kiwon lafiyaCututtuka da kuma Yanayi

Rasmussen ya cutar (encephalitis). Dalilan Rasmussen ciwo

Rasmussen ya cutar nasa ne da category na rare kumburi cututtuka watse daga cikin kwakwalwa. Wannan encephalitis yakan auku a yara a karkashin shekaru 15. Mafi sau da yawa, da rashin lafiya da aka yi fama da tsufa. A matasa da kuma manya, irin wannan encephalitis ne sosai rare.

A tsari ya shafi daya ko sauran yammancin duniya na kwakwalwa. Kamar yadda cutar progresses, likitoci lura da shi m atrophy. Doctors nuna zuwa matsananci jure cutar jiyya. A gaskiya ma, cikin Rasmussen cuta - encephalitis tare da takamaiman siffofin da cewa ba za a iya warke.

M haddasawa encephalitis Rasmussen

Up har da etiology da cutar ba a kafa. Masana kimiyya ne kawai gano uku key dalilai da za su iya fara da raya ci gaban mai pathological yanayin tasowa a cikin tsakiya m tsarin. A jam'i na likitoci yi imani da cewa Rasmussen ciwo ne ya sa ta autoimmune antibodies, ƙwayoyin cuta da kuma cytotoxic T-lymphocytes.

Zai yiwu rawar da cytomegalovirus, wanda aka ware daga cerebral bawo na adult marasa lafiya. Yana yiwuwa cewa wadannan pathogens sa kumburi, masu tasowa, a cikin wani m rashin lafiya. Bugu da kari, shi za a iya precipitated rikitarwa bayyana bayan kafin kamuwa da cuta.

Yanzu, mafi masana kimiyya yi imani da cewa shi ne wani autoimmune antibodies hanyar encephalitis Rasmussen. A Sanadin cutar kuma ya yi ĩmãni da za a bayyana ta cytotoxic T-lymphocytes.

A marasa lafiya da Rasmussen ta ciwo, wani lokaci ana samu tsakanin dangi suka sha wahala daga sauran autoimmune cututtuka. Alal misali, Behçet ta cutar. Wannan ya nuna da suke cewa zumunta suna da hannu a cikin pathological tsari na kowa kayyade al'amurran. A musamman, shi ake magana a kai dalilai kamar Hla-galotipy.

Symptomatology entsifalita Rasmussen

Da farko, cutar bayyana mai da hankali motor seizures. Kamar yadda cutar harin ya shiga gida myoclonus. A tsawon lokaci, da hare-haren tsananta. Suna tare da tsoka spasms, asarar sani da kuma fall. Sau da yawa, marasa lafiya fuskanci hare-hare a lokacin barci.

Ci gaba, cutar bayyana kanta asarar ƙarfi, kuma m numbness da ke faruwa a kowane bangare na jiki. Nazarin ya nuna wani karu a aiki a shafa kwakwalwa yankin.

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Alamun furta a cikin mutane da wahala na shekara da kuma wani ciwo na Rasmussen. Encephalitis da etiology na kokarin gano a farkon yiwu. Wannan yale mu mu fatan for kyau sakamakon immunosuppressive far. Saboda haka na farko na duk koma ga nazarin asibiti, MRI da EEG aka yi.

Hanyoyin da magani daga Rasmussen ta encephalitis

Saboda haka yanzu akwai rigingimu game da Sanadin Rasmussen ta ciwo, encephalitis ba a bi ta al'ada hanyoyin. Idan farkon ganewa na cuta rubũta antiepileptic magunguna hali. Bayar da shawarar a rage cin abinci tsara ƙara da amfani da abinci mai arziki a cikin kitse, kuma a rage a cikin adadin rage cin abinci abinci dauke da carbohydrates. Sau da yawa ga ya da amfani don amfani plasmapheresis, corticosteroids, immunoglobulins.

Sau da yawa, da lura da cutar sun koma ga m hanyoyin. Marasa lafiya da suka sha wahala rashin lafiya mai tsanani da kuma hadadden kwakwalwa rauni, wajibi ne a yi transplants na jijiya Kwayoyin. Yanzu har zuwa yiwu mu yi kokarin ba da za su gudanar craniotomy.

Wani lokaci marasa lafiya miƙa m baki - Hemispherectomy. Bayan shi ya fi sauƙi ga Rasmussen ta ciwo. Encephalitis, ba shakka, ya fita da burbushi, pronounced paresis ko matsaloli tare da jawabin. Duk da haka, kai hari da haƙuri ne ƙasa da na kowa.

Don daina tiyata ne ba kyawawa, duk da cewa shi ba ya haifar da kammala waraka. Bayan duk, ci gaban da cutar aggravates m neurological gaira, da wanda akwai shafi tunanin mutum retardation kuma inna.

A lokuta da hadin raunuka na kwakwalwa (duka hemispheres) Hasashen rashin alheri ya fi karfinsu. Lokuta da mutuwa tsakanin marasa lafiya da encephalitis Rasmussen ke ba nadiri.

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