Kiwon lafiyaShirye-shirye

Me kuke kira mafi tsada magani a duniya?

Kudaden shiga na wasu pharmaceutical kamfanonin birgima a kan wani biliyan. Wannan shi ne saboda cewa su isar da tsada da kwayoyi, samar a kananan batches. Yawanci wannan magani, kauce wa m pathologies. Wasu masana sun yi imanin cewa kudin da wasu magunguna ne da muni saboda gaskiyar cewa babu wani gasar. A jerin irin kayayyakin ne quite m, daga gare su, mafi tsada a duniya da magani zai kudin fiye da miliyan kudin Tarayyar Turai.

Da miyagun ƙwayoyi Aldurazyme

Wannan magani an tsara su bi Hurler ciwo, wanda bayyana kanta a cikin shimfiɗar jariri. Ta shan wahala daga wani rashin lafiya kadan fiye da ɗari shida da mutane a dukan duniya. Rashin lafiya damuarn jiki da kuma halin kirki ci gaban yara a matsayin matasa kamar shekaru hudu da haihuwa.

The kudin na wannan makaman ne kamar dubu ɗari biyu daloli.

Drug "Cerezyme"

A wani kudin na wannan magani zai kudin game da wannan adadin a matsayin Aldurazyme. "Cerezyme" -, daidai ne a matsayin mafi tsada magani a duniya. Kuma an wajabta, Gaucher cuta. Domin da cutar halin da jari na m adibas a cikin huhu, hanta, kwakwalwa da kuma bargo. Wannan irin Fading kiba rikitarwa aiki na huhu da kuma kodan. Magani ya sauya enzyme cewa shi ne a Gaucher cuta ne gaba daya fakowa ba.

Ko'ina cikin duniya, mutane da wannan ciwo game da shida da mutane dubu.

Da miyagun ƙwayoyi Myozyme

Akwai game da daruruwan kwayoyi, wanda kudin fiye da dubu kudin Tarayyar Turai ta vial. Duk wadannan kwayoyi kasance a cikin category na "mafi tsada magani a duniya." Mene ne sunan wani miyagun ƙwayoyi a cikin wannan kungiya? Wannan magani Myozyme, domin lura da Pompe ciwo. A Pathology halin da rashi na alpha-glucosidase. Wannan take kaiwa ga hallaka tsokoki da kuma kaifi karuwa a cikin juz'i na zuciya, ci gaba na numfashi Pathology. Mafi sau da yawa, da rashin lafiya da aka gano a cikin shimfiɗar jariri.

Da yin amfani da miyagun ƙwayoyi iya dakatar da matakai da kuma taimaka yara fara numfashi da kansa. A kudin jiyya wakili zai kudin ɗari da dubu kudin Tarayyar Turai domin yaro. Idan cutar da ake bincikar lafiya a} uruciyarsa, sa'an nan magani zai dauki fiye da dubu ɗari uku.

yana nufin Fabrazyme

Wani mafi tsada magani a duniya - shi ne a wajen Fabrazyme. A kudin miyagun ƙwayoyi jiyya zai kudin game da dala dubu xari uku.

Da miyagun ƙwayoyi ci gaba domin lura da Fabry cuta. Ana sa a kona abin mamaki, wani kara girman zuciya, koda matsaloli. A duniya, mutanen da fama da wannan cuta, babu fiye da dubu uku mutane.

Da miyagun ƙwayoyi Arcalyst

Wasu yi imani da cewa mafi tsada a duniya da magani - wani magani m Regeneron kira Arcalyst, domin lura da ciwo Muckle-Wales. Pathology ne maimaituwa intermittent zazzabi, hadin gwiwa zafi, koda. Cuta rinjayar game da miliyan biyu da mutane a dukan duniya.

A kudin da miyagun ƙwayoyi ne game da mutum ɗari biyu da ashirin da dubu daloli.

Da miyagun ƙwayoyi Soliris

Wasu lokaci da suka wuce, mafi tsada magani a duniya - Soliris. A farashin da miyagun ƙwayoyi daga game da rabin miliyan daloli. Yana nufin zalunta a cuta a cikin abin da na rigakafi da tsarin halaka ja jini Kwayoyin. Wannan magani an dauka game da maza dubu biyar.

Magunguna da kuma Elaprase Naglazyme

Wani magani daga category daga cikin mafi tsada magani a duniya - ne mai magani Elaprase. Its kudin ne ɗari huɗu da dubu daloli. Yana nufin nuna ga Hunter ciwo. Domin pathologies halin da wata karuwa da harshe, kwakwalwa lalacewa da kuma smoothed hanci. Duniya, wannan magani daukan game da dubu biyu da mutane.

Aƙalla guda kudin Naglazyme. Kuma an wajabta, mu bi Maroto-Lamy. Syndrome rinjayar fiye da dubu mutane a duniya. Domin da cutar halin m lebe, short jiki da kuma manyan kai. Riga daga shekara goma sha biyar, marasa lafiya tsare a keken hannu.

Cinryze

Wannan magani - mafi tsada magani a duniya da kuma daraja fiye da dala dubu xari uku. Da miyagun ƙwayoyi da aka tsara don yi wa hereditary angioedema irin. A wannan rashin lafiya bayyana illa rigakafi da tsarin, sa mai tsanani kumburi na lebe, kogon ciki.

A mafi tsada magani

Saboda haka abin da ke cikin mafi tsada magani a duniya? Nawa ne kudin? Biyu kamfanonin ketare sun ci gaba da ya fi tsada magani a duniya. Glybera shi ne ake kira. A kudin magani wannan ginin zai zama fiye da miliyan kudin Tarayyar Turai.

New gene magani ne aka yi nufi ga yi wa wani rare kwayoyin cuta - lipoprotein lipase rashi. A enzyme shirya matakin na lipids a cikin jiki. Saboda gene maye gurbi enzyme ba samar da jiki, saboda yana da wani babban hadarin jijiyoyin bugun gini occlusion.

Daya vial da miyagun ƙwayoyi za kudin fiye da dubu hamsin Yuro, da kuma cikakken hanya na lura da cutar zai zama fiye da miliyan. Mai yiwuwa marasa lafiya tare da wannan ciwo, akwai game da ɗari biyu da mutane a Turai, don haka da kayan aiki ne mai wuya a yi wani tasiri a kan kasafin kudin na kiwon lafiya cibiyoyin.

Duk da babban price, da kayan aiki ne iya gaba daya warkar da Pathology. Bisa ga Developers, da hanya na lura da rahusa mahara enzyme maye far.

Da miyagun ƙwayoyi Glybera gene ne na huɗu makaman a duniya. Biyu na farko da aka ci gaba da American masana kimiyya da kuma samar a kasar Sin. Dukansu kayan aikin an tsara domin lura da ciwon daji, wato, cutar sankarar mahaifa da marurai na shugaban. Uku nufin a Rasha. Wannan kayan aiki ne da ake kira "Neovaskulgen", akayi nufi don lura da ƙananan reshe ischemia. A hanya na lura da wannan magani zai kudin game da ɗari uku da dubu rubles.

Biotechnological hukumomin yi imani da cewa mafi tsada kwayoyi a duniya, photos na wanda za a iya samu a cikin labarin kuɓutar da kanta. A gaskiya, har sai da zuwan wadannan kwayoyi, mutane da yawa fama da mummunan pathologies, sami ikon rabu da su ailments. Pharmaceutical kamfanoni su ne m sayar da wadannan kwayoyi, tun da talla ba bukatar kashe kudi. Har ila yau, wadannan kwayoyi ne kusan babu gasar, da sa masana'antun kansu ƙayyade da kudin da miyagun ƙwayoyi da kuma ta kasancewa.

A Amurka kamfanonin inshora maida kudin da tsada kwayoyi ga marasa lafiya, da kuma wasu masana'antun bayar da free magani mabukata.

Masana a duk faɗin duniya ya baratar da babban kudin sabon kwayoyi. A cewar su, da yin amfani da irin wannan magunguna da damar da yawa marasa lafiya partially, da kuma a wasu lokuta dawo gaba daya yin kawar da m syndromes. Masana sun yi imani da cewa farashin wadannan kwayoyi ya rage, gasar da ake bukata. Kawai 'yan mutane zaton waɗanda suke sun gano tsanani cuta, kuma ko da a wani wuri shekaru, suna da kamar wuya a iya saya da kwayoyi, costing dubbai. A mafi yawan lokuta, mutane ba su da damar da za su saya da irin wannan tsada magunguna.

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