Klippel-Trenaunay ciwo: photo, cututtuka, magani

More jam'i cututtuka kafa tayi lokaci. Saboda haka, da tasiri a kan su ci gaba da iya ba ko da yaushe. Bayan duk, mafi yawan wadannan munanan ake bincikar lafiya ne kawai bayan da yaro ta haihuwa. Kuma wasu da yawa daga baya. Don daya daga cikin kwayoyin cututtuka kamata hada Klippel-Trenaunay cuta. A ciwo aka gano a cikin farkon karni na 20th. Wannan ne dangana zuwa fitowan da wani ilmin halittar jini. Sau da yawa cutar saukin kamuwa maza. Duk da haka, shi kuma an samu daga cikin mace yawan jama'a. Pathology dangana ga nakasar jijiyoyin bugun gini cuta.

ciwo, Klippel-Trenaunay Description

Klippel-Trenaunay ciwo ne dauke da wani m kayyade lahani. Hango da ci gaban wannan Pathology ne kusan yiwu ba, saboda aibi ne m, kuma shi ba a gano cutar a lokacin daukar ciki. Duk da haka, a wasu lokuta, cutar za a iya zargin Klippel-Trenaunay. A ciwo tana nufin wani hereditary cuta. Saboda haka, kwayoyin analysis ya zama batun mata masu ciki a wani iyali inda lokuta wannan cuta ya faru. Wani sunan da cutar - hypertrophic hemangiectasia. The asibiti hoto Klippel-Trenaunay ciwo ya hada da uku babban bayyanar cututtuka:

1. Varicose veins.
2. A bayyanar shekaru spots a kan fata.
3. Canza fadi da tsawon da abin ya shafa reshe.

A wasu lokuta na kwarangwal da kuma taushi nama hypertrophy aka kiyaye. Sau da yawa Pathology halin da m hanya. A hangen nesa ya dogara da tsanani daga jijiyoyin bugun gini canje-canje. Ko da yake cikin hanyar cutar ba za a iya shafe ta, warkewa matakan taimaka inganta ingancin rayuwa na haƙuri. Mutane fama da wannan cuta da aka sanya a tawaya.

Sanadin Klippel-Trenaunay ciwo

Domin wasu dalilai, akwai wata cuta a Klippel-Trenaunay? A ciwo tasowa a sakamakon wani kayyade lahani. Wannan anomaly yana daukar kwayar cutar a cikin wani autosomal rinjaye gado irin. Wannan yana nufin cewa idan akwai irin wannan kwayoyin aibi a daya daga cikin iyaye, akwai yiwuwar na ciwo a wani yaro ne 50%. Har ila yau, cutar za a iya daukar kwayar cutar ta hanyar daya tsara, cewa shi ne - daga kakaninki. A wannan yanayin, yiwuwar ne 25%.

Kamar dukan kayyade munanan, jijiyoyin bugun gini lahani ci gaba a lokacin da fetal nama alamar shafi. Yana iya shafar tareda žata effects. Wadannan sun hada da dalilai kamar:

1. M rashin jin daɗi a makanni kadan da farko na ciki.
2. Cututtuka. Na bayar da muhimmanci ne na kullum kwayar raunuka na jiki.
3. Da amfani da kwayoyi tare da teratogenic Properties.
4. Kudin shiga kwayoyi jim kadan kafin ganewa da kuma a lokacin daukar ciki.
5. Shan taba da kuma shan barasa.
6. Air gurbatawa da guba abubuwa, radiation.

Dukkan wadannan abubuwan zai iya sa canje-canje a cikin jikin mata da ba a haifa ba. Su ne musamman m, a farkon matakai na ciki. Bayan daban-daban anomalies za a iya generated a cikin wannan lokaci.

Hanyar cutar

Me akwai jijiyoyin bugun gini canje-canje a cikin cuta Klippel-Trenaunay? A ciwo bayyana ãyõyi na venous cuta. Ginshikai na cin gaban Pathology da tarewa da outflow na jini daga cikin ƙananan extremities. Wannan shi ne saboda gaskiyar cewa venous lumen aka quntata, akwai wani matsawa na jijiya reshe jirgin ruwa, hypertrophied tsoka, saura tayi nama. Saboda take hakki na da outflow na jini akwai hauhawar jini. Vienna ne a hankali thinned, da fallasa su lalacewa. Bugu da kari, disrupted aiki na bawul na'ura. Saboda jini stasis reshe fara hypertrophy. Saboda da stagnation sha wahala trophic aiki. Saboda haka, nama da fallasa su ischemia. Tsawo tashin hankali na jini wadata take kaiwa zuwa sclerosis. Haduwar jijiyoci mai taushi hypertrophy auku hyperemia da edema. A wasu lokuta, su ne batun canza da kuma kasusuwa. Saboda haka stunned da wani reshe na iya ba kawai kara a fadin, amma kuma tsawaita.

Klippel Trenaunay Syndrome-: cututtuka

By da manifestations Klippel-Trenaunay ciwo hada da canje-canje ba kawai a kan wani ɓangare na venous tsarin, amma sauran lahani. Duk da cewa nakasar abnormality, na farko bayyanar cututtuka za su iya bayyana a samartaka ko ƙarfinsa. Saboda haka, na asibiti manifestations hada da wadannan take hakki:

1. Dilation na waje kafar jijiyoyinmu. Yana bayyana pathological kinking da zafi tare da jirgin ruwa bayyane zuwa ga tsirara ido. A mafi yawan lokuta varicose veins located a kan m surface na kafafu.
2. A karuwa a cikin adadin reshe. Sau da yawa tare da kumburi events. Saboda jini stasis shafi kafar iya zama sosai daban-daban daga m reshe. Sau da yawa shi ne hyperemic, thickened fata.
3. Reshe tsawon kwanakinka. Hypertrophy iya Dukan ƙafafunsa da hannuwansa.
4. A bayyanar pigmented nevi a kan fata. A wani hanya, wadannan tsarin ake kira "ruwan inabi stains".

Har ila yau, tare da ci gaban da cutar bayyana trophic canje-canje. ulcerative lahani na iya faruwa a shafi yankunan, wanda ba warkar da na dogon lokaci. Da sauran munanan tasowa a cikin wannan Pathology, akwai polydactyly, gaban Fused juna yatsunsu ko yatsun kafa.

Yadda za a gane asali cutar Klippel-Trenaunay?

Syndrome ganewar asali Klippel-Trenaunay ne sau da yawa dangane da asibiti manifestations. Alamun cutar bayyana a hankali. A farko alamar iya zama bayyanar "ruwan inabi stains" ko jijiyoyinmu. Idan wadannan cututtuka ake hada da hypertrophy na reshe fallasa ganewar asali: Klippel-Trenaunay ciwo. Photos of mutanen da fama da wannan cuta ne kama da juna. Su za a iya gani a cikin adabi kishin rare kayyade pathologies. Saboda haka, mafi ganewar asali ne ba wuya.

Bugu da kari ga na asibiti data, yi venography, ultrasonography daga cikin ƙananan wata gabar jiki, X-haskoki.

Klippel Trenaunay Syndrome-: magani daga cuta

da aiki yana dauke da manyan likita taron. A girma daga baki ne m da mataki na jijiyoyin bugun gini rauni. Don fadada lumen na jijiya stenting aka yi. Lokacin da wani babban yanki na halaka samar kewaye jirgin ruwa - sauya shi da wani implant shafin.

Don magance varicose nada skleroteropiya, Laser coagulation na jijiyoyinmu. Marasa lafiya fama da wannan cuta dole ne sa matsawa tufafi.

ciwo, Klippel-Trenaunay Rigakafin

Klippel-Trenaunay ciwo a jarirai yana da wuya kamu. Sau da yawa shi ne gano a cikin watannin farko, ko shekaru na rayuwa. Don hana cutar, da shi wajibi ne don kare kansu daga cutarwa effects a lokacin daukar ciki. Wani m gwargwado aka dauke su a kayyade jarrabawa da tayin a gaban lokuta da cuta a cikin iyali.