Mauriac ciwo a ciwon sukari

Mauriac ciwo - wata cuta da cewa tasowa a matsayin mai wahala saboda rashin lura da ciwon sukari a wani matasa shekaru. Domin da farko lokacin da cutar da aka bayyana a cikin 1930 da Faransa likita Pierre Mauriac asalin. Ya bayyana irin na asibiti hoto a wadda yara fama da ciwon sukari da kuma insulin far da ba daidai ba sashi, motsa jiki da wasu waje ãyõyi. Ya lura cewa, duk da yara ne irin wannan a cikin bayyanar, wanda aka nuna a cikin low girma, kiba, retarded jima'i ci gaba.

A Sanadin cutar

Babban dalilin da tsanani da rikitarwa shi ne ba daidai ba biyã ciwon sukari far. A wannan cuta da pancreas ba aiki da kyau, ba samar da isasshen yawa na insulin. Saboda da Pathology auku glucose kasawa a cikin Kwayoyin saboda da cewa shi fi mai da hankali a yawa a cikin jini.

Mauriac ciwo ci gaba a marasa lafiya da ciwon sukari mellitus irin 1 ake dangantawa da rashin magani. Marasa lafiya yaro na dogon lokaci kasa insulin kashi gudanar, ko amfani da kayayyakin da low quality, kuma bad tsarkakakku, abu zuwa kullum rashi na insulin.

Tsawo rashin insulin a cikin jiki take kaiwa zuwa da wadannan matakai:

• Rayuwa cuta, musamman da cuta daga carbohydrate metabolism.
• Kara girman da hanta da kuma ta m degeneration saboda ya karu glycogen fashewa.
• Canje-canje a cikin jini abun da ke ciki - karuwa a jini glucose, cholesterol, m acid.

Idan wannan shi ne ba duk pathological tafiyar matakai a cikin jiki a lokacin Mauriac ciwo, kuma yara marasa lafiya fuskanci wadannan sabawa:

• Ƙarancin samar da muhimmanci hormones - cortisol, girma hormone, glucagon, kuma saboda abin da wani take hakkin da ci gaban tsarin.
• Fashewa sunadaran da kuma arziki fitarwa alli da phosphorus daga ƙasũsuwa, ƙarshe abu don ci gaban osteoporosis da kuma wasu tsoka atrophy.
• Rashin iyawa sha na bitamin a cikin hanji.

Cutar yawanci bayyana kanta tsakanin zamanai na 15-18 shekaru, amma dysfunctional aiwatar fara yawa a baya. A halin yanzu, domin lura da farkon m yana amfani da zamani da kuma sosai tsarkake shirye-shirye, wanda kusan gusar da cin gaban Mauriac ciwo.

symptomatology da cutar

Mauriac Syndrome ciwon sukari yana da yawan abubuwan:

• The yaro lagging a baya a ci gaba da kuma ci gaban hanawa. Sau da yawa akwai kiba da gajeren jiki. A wannan yanayin, wani m yaro iya wanzuwa da takwarorinsu a cikin ci gaban da 10-30 santimita.
• A fada a jima'i ci gaba (underdeveloped jima'i halaye da kuma babu haila a 'yan mata).
• Protracted mafarki.
• Kiba, musamman a fuskar da babba jiki tare da bakin ciki wata gabar jiki. Marasa lafiya yara suna kama, da "jinjirin wata-dimbin yawa" a juna ta fuskar, short wuyansa, kitse a cikin makamai, kafadu, ciki. Ƙananan sashi na jiki ne na bakin ciki sosai.
• Karuwan hanta tare circuitous venous wurare dabam dabam.
• Osteoporosis (inda hakan ya saukar da ci gaban kashi nama).
• ido cututtuka, ciki har da cututtuka na akan tantanin ido, kuma baya ci gaban da cataracts.

Mafi na kowa Mauriac ciwo a cikin yara, da marasa lafiya yaro photo nuna abin da cututtuka da cutar.

ganewar asali da cutar

A ganewar asali da "Mauriac ciwo" da aka kafa a fili na waje alamu da cutar, kamar: rashin tsawo ga shekaru, gaban kiba, musamman a fuskar jima'i rashin ci gaba, bayyananne karuwa a cikin hanta.

Don tabbatar da ganewar asali da za'ayi jini gwaje-gwaje, wanda a cikin sa da wadannan manifestations ne:

• m glucose matakan, don nuna m tsalle a cikin babban, sa'an nan down.
• Wuce kima jini lipids (hyperlipidemia).
• A gagarumin karuwa a jini cholesterol matakan (hypercholesterolemia).

A wasu lokuta, kara nazarin hanta biopsy ga wannan dalili, su fitar da mai kaya

cutar

Ga matasa jiki da cuta ne musamman wuya. Kamar yadda mai tsanani nau'i na ciwon sukari, yana da wuya a rama domin. Sau da yawa yana sa acidosis da hyperglycemic coma.

Mauriac ciwo ya auku a cikin tsanani saboda m Bugu da kari na daban-daban cututtuka, kazalika da hadaddun da dogon dawo da biochemical matakai a cikin jiki.

Mauriac ciwo da kuma Nobekura: Kamance da kuma bambance-bambance

Mauriac ciwo da kuma Nobekura sau da yawa tasowa a cikin shimfiɗar jariri, da cututtuka ne mai tsanani wahala da ciwon sukari da ya auku a kan wani bango na m magani. Dukansu syndromes da irin wannan bayyanar cututtuka, da suka hada da ci gaban retardation da kuma jima'i ci gaba, a protracted samartaka, m hanta. A wannan yanayin, babban bambanci Nobekura ciwo ne rashin wuce haddi jiki mai. A wannan yanayin, da magani daga duka biyu syndromes da nufin rauni da magani na ciwon sukari.

Mauriac ciwo magani

Direct magani na ciwo kamar wannan ba ya wanzu. All far da nufin magance tushen Sanadin cutar da kuma matsalolin da lalacewa ta hanyar su. Don yin wannan, da haƙuri da aka sanya wa daidai insulin far a daidai sashi da kuma ingancin da zamani kwayoyi.

Don hana lipodystrophy gudanar da wani yawan m hanyoyin da wannan manufa nada a matsayin tausa, physiotherapy da Charts ga insulin injections. musamman rage cin abinci za a iya sanya a Bugu da kari ya magani, an cire daga cikin abinci dukan abinci dauke da dabba fats. A wannan yanayin, da rage cin abinci mayar da hankali a kan furotin da kuma carbohydrate abinci.

Medical far an kuma tsara don rama ci gaba a kan bango na tamkar cuta da rikitarwa ga wannan haƙuri naznachetsya:

• Kudin shiga gepatoprotektorov don mayar da hanta Kwayoyin.
• B bitamin maido da metabolism.
• Complex miyagun ƙwayoyi da nufin maido da martabobin lipids da cholesterol a cikin jini.
• Steroid kwayoyi zuwa fararwa da jiki ta girma.
• Hormonal kwayoyi don mayar da muhimmanci jima'i ayyuka.

Yin rigakafi da hangen nesa

Don hana wannan hatsari wahala na ciwon sukari kamar yadda Mauriac ciwo, shi wajibi ne a gudanar da wani daidai magani daga tamkar cuta da kuma hana insulin rashi.

Lokacin da hada magani ya riga ya ci gaba da ciwo zamani kwayoyi hangen nesa m isa, amma idan duk likita ta shawarwari. A daidai sashi na insulin da mayar da ayyuka na duk gabobin shafa sun iya komawa da yaro ta kiwon lafiya, duka waje da ciki.