Sideroblastic anemia: cututtuka, magani

Mutane da yawa san cewa anemia ne mai matukar hatsari cutar. Akwai su da yawa irin wannan cuta, kuma kowane daga cikinsu shi ne cutarwa ga lafiyar dan adam. Sideroblastic anemia ne mai hadarin gaske Pathology dangantawa da sosai microelements kira. A wannan cuta da bargo ta amfani da baƙin ƙarfe haemoglobin jam'iyya, don haka ne ajiyar a ciki gabobin. Babban abu - don hana rikitarwa, kuma domin wannan dalili ya kamata a da sauri neman sana'a taimako.

ra'ayi

Sideroblastic anemia bambanta daga wasu irin cututtuka rage taro na baƙin ƙarfe a cikin ja Kwayoyin. Gaskiyar cewa bargo ba ya amfani da wannan kashi a cikin kira na haemoglobin. Mafi sau da yawa, da rashin lafiya tasowa kamar nakasar ko samu. A kayyade matakin, anemia faruwa da mafi yawa a boys.

A cutar za a iya daukar kwayar cutar a matsayin autosomal rinjaye hanya. Wannan ake kira anemia ciwo Pearson. Lokacin da jiki ne talauci tunawa da baƙin ƙarfe, shi ne ajiyar a ciki gabobin, sakamakon sideroblastic anemia. Idan gland shine yake zama da yawa, da aikin da aka karya hanta, koda da kuma zuciya tsoka.

iri cututtuka

Wannan irin anemia aka raba da mataki na mai tsanani, amma kuma saboda bayyanar da na asibiti hoto. Da dama jinsin iri sideroblastic anemia:

1. Hereditary. The rashin lafiya da aka gada a sakamakon gene maye gurbi. Wannan ya haddasa anomaly Pathology na rayuwa aiwatar shafe bitamin B6 da aminolevulinic acid. Cutar da ke sa kansa ya ji bayan haihuwa ko a lokacin samartaka.
2. Nakasar. Wannan nau'i ne ware daban, ko da yake a wasu har shi da dangantaka da hereditary form. A nan, halin da babban abun ciki na erythrocyte coproporphyrin.
3. An samo. Yana bayyana a sakamakon da illa na sinadarai. Daga cikin su akwai ethanol, gubar, tsiklosirin.

Matsaloli tare da baƙin ƙarfe kira ma faruwa saboda ƙari matakai a cikin jiki. Aƙalla 1/10 da marasa lafiya da sideroblastic anemia shan wahala daga m cutar sankarar bargo.

Sanadin cutar

A farko dalili da cuta ne da rashin protoporfiirina, wanda shi ne daya daga cikin mafi muhimmanci da aka gyara na kira na haemoglobin kashi. Bugu da kari, abubuwa da hannu a cikin halittar mafi gina jiki da na baƙin ƙarfe.

An samo form sideroblastic anemia taso ne daga gaskiya cewa jiki ba ya shigar da zama dole abubuwa a wani isasshen adadin. Akwai yanayi inda ake so fili an suppressed da magunguna da cewa daukan mutane.

The jiki ne tsautsayi a sakamakon daukan hotuna zuwa barasa. Anemia iya faruwa saboda gubar dalma ko liyafar da karfi maganin rigakafi. A hereditary nau'i ne ratsa mace chromosome lalace genome. Har ila yau, a cikin hanyar cutar na iya zama wani rashin lafiya na rigakafi da tsarin da kuma ci gaban neoplastic tafiyar matakai.

Ganewar asali sideroblastic anemia

A tsari na gano cutar ne quite hadaddun, tun da shi fitowa kusan asymptomatic. Bugu da ƙari, akwai wani jinsin na asibiti hoto, wanda za ka iya dogara. Idan ka duba kawai a waje da ãyõyinMu, da ganewar asali da wannan cuta ne na gaskiya ba. Duk da haka, akwai hanya daya don gane sideroblastic anemia - wani jini gwajin.

Har ila yau, gudanar da aiki da jarrabawa na ciki gabobin na haƙuri, to sami baƙin ƙarfe adibas. Amma da lokaci kashi, don haka shi ya sa hematological bayyanar cututtuka. Don kauce wa kuskure, wajibi ne a tabbatar da ganewar asali. Wannan ne yake aikata tare da taimakon wani macroscopic nazarin bargo.

Domin cewa hadarin da aka rage girmanta, shi wajibi ne don gudanar da wani biopsy. Yana da wannan hanya shi ne mafi inganci hanya domin sanin sideroblastic anemia. Yana yana da za'ayi kamar haka: pre-stained biopsy na musamman abu, kuma idan gano ba-hada da baƙin ƙarfe, wakilin mahadi zama a bayyane.

Don abin da gwani don magance?

Kamar yadda muka rigaya muka gani, da bayyanar cututtuka na anemia sideroblastic kusan m. The asibiti hoto ne kuma m, kuma saboda cewa akwai wasu matsaloli. Idan mutum ya ji gajiya, mãsu rauni a jiki, shi yawanci tana nufin ilimin. A likita mutanen da ake zargin anemia gaba da mãsu haƙuri a hematologist wanda aka gudanar da wani binciken.

Na farko, da gwani ya sami janar jihar na haƙuri shi ne sha'awar salon, miyagun halaye, a jerin cututtuka da kuma dakatarda t. D. Idan likita deems zama dole, zai rike da dama da karatu. Wadannan sun hada da:

• jini (da kuma biochemical).
• hanta biopsy.
• bincike na bargo cell abun da ke ciki.

Hematologist iya optionally shiryar da mãsu haƙuri ga sauran kwararru domin karin cikakken jarrabawa. Alal misali, a sami wani nau'i na anemia, shi wajibi ne don jũya zuwa ga halittar jini. Wannan likita zai ƙayyade ko akwai zama wani hereditary nau'i na sideroblastic anemia. Yana iya ma bukatar tuntubar wani likitan mata, urologist ko proctologist.

Hanyar magani

Kafin ka fara jiyya, dole ne ka ƙayyade ko akwai lalle ne, haƙĩƙa baƙin ƙarfe shaida. A saboda wannan dalili, desferalovuyu samfurin. An gudanar da intramuscular allura, da kuma sakamakonsa na fitsari ya kamata a kasaftawa kamar 0.5-1.1 MG na baƙin ƙarfe, da kuma a hypochromic, gipersideremicheskoy, sideroahrestical, sideroblastic anemia - 5.10 MG.

Shi ne ya kamata a lura da cewa hereditary nau'i na cutar ba za a iya warke. Don kashe gene wanda ya fara zuwa mutate akai-akai used magani da high allurai bitamin B6. An gudanar a wani adadin na 100 MG da rana. Duk da haka, da dauki na jiki ne kusan unpredictable. A lura da sideroblastic anemia haemoglobin matakin ya tashi zuwa al'ada matakan a cikin watanni uku. Idan a lokacin wannan lokaci ba ya taimaka, m m far.

Yin rigakafi da hangen nesa

Popular sau da yawa, cutar na faruwa a sakamakon gubar dalma. Don hana wannan, kula dole ne a dauki ga magance wannan al'amari. A lokacin da maimaitawa na tsohon gidaje bukatar daukar sauna kamar yadda zai yiwu ga dan lokaci resettle yara. Kada a jefa, ko kuma rufe Paint dauke da gubar. Shi ne mafi kyau ga kankara kashe ko cire su chemically. Bugu da kari, da bukatar a kai a kai saka idanu da m na gabatarwa, bi da ginin da kuma kiwon lafiya nagartacce.

Warkar da hereditary nau'i na cutar ba zai yiwu ba. Domin tabbatar da amfani effects bukatar kullum saka idanu da jini kirga, musamman da matakin na haemoglobin. Wannan aka samu da na yau da kullum da nassi daga tafarkin far, wanda ba ya ba da damar da cutar wajen samar da kuma kula da al'ada yanayin mutum.